0:00:04 > 0:00:07Tonight at 6pm - Six months after the Grenfell Tower fire,
0:00:07 > 0:00:16a memorial service at St Paul's.
0:00:16 > 0:00:18SINGING.
0:00:18 > 0:00:21A community comes together today, just as it did in the aftermath
0:00:21 > 0:00:26of that June night, and, still, there are questions.
0:00:26 > 0:00:30Today, we ask why warnings were not heeded, why a community
0:00:30 > 0:00:38was left feeling neglected, uncared for, not listened to?
0:00:38 > 0:00:41Honouring the lives of the 71 victims - we hear
0:00:41 > 0:00:43from survivors and relatives.
0:00:43 > 0:00:51It was comforting to know that people still remember them,
0:00:51 > 0:00:54and share our grief and talk about it.
0:00:54 > 0:00:59We'll be hearing from one family, finding out how they've coped.
0:00:59 > 0:01:02Also tonight, for the first time, Scotland has different tax rates
0:01:02 > 0:01:04to the rest of the UK - low earners pay less,
0:01:04 > 0:01:08higher earners pay more.
0:01:08 > 0:01:09Theresa May joins EU leaders in Brussels -
0:01:09 > 0:01:11and admits she's disappointed
0:01:11 > 0:01:15about last night's Brexit defeat in the Commons.
0:01:15 > 0:01:18Rupert Murdoch spent a life time building a media empire -
0:01:18 > 0:01:24now he's sold most of it to Disney.
0:01:24 > 0:01:26And, imagine, every time Jake took a walk, he took
0:01:26 > 0:01:29a risk with his health - now there's new hope
0:01:29 > 0:01:35for haemophillia patients like him.
0:01:35 > 0:01:40And coming up on Sportsday on BBC News, a strong start for England in
0:01:40 > 0:01:45the Ashes Test they must not lose. 305-4 after day one with a maiden
0:01:45 > 0:01:58test century for Dalwood Mallan. -- Dawid Malan.
0:02:02 > 0:02:08Good evening and welcome to the BBC News at Six.
0:02:08 > 0:02:11Six months after the Grenfell fire, survivors and relatives of the dead
0:02:11 > 0:02:14were joined by hundreds of others, including members of the Royal
0:02:14 > 0:02:21family, for a memorial service at St Paul's.
0:02:21 > 0:02:2371 people - 18 of them children -
0:02:23 > 0:02:26died on the night of June 13.
0:02:26 > 0:02:29For many, the disaster has come to symbolise the huge disparity
0:02:29 > 0:02:32between rich and poor in one of London's wealthiest boroughs.
0:02:32 > 0:02:35Speaking at the service, the Bishop of Kensington asked why so many
0:02:35 > 0:02:37in the community have been left feeling neglected.
0:02:37 > 0:02:42Here's our Home editor, Mark Easton.
0:02:42 > 0:02:46BELLS.
0:02:46 > 0:02:50They came to St Paul's, to mourn those who were lost, to comfort
0:02:50 > 0:02:56those who still suffer, and to thank those who worked to heal.This is
0:02:56 > 0:03:04the family we lost, five people.On the 21st floor?On the 21st floor,
0:03:04 > 0:03:12yes.How important is this event to you?Very important.Anything to
0:03:12 > 0:03:17remember them is important, for us. Every strand of British cultural
0:03:17 > 0:03:22life was woven into a service of remembrance, community and hope.
0:03:22 > 0:03:30Grenfell survivors, family and friends, politicians and royalty.
0:03:30 > 0:03:34The Grenfell fire exposed deep social divides in modern Britain.
0:03:34 > 0:03:40This morning, here at the cathedral, those destined to inherit a kingdom
0:03:40 > 0:03:46stand beside those who have lost everything from from highness to
0:03:46 > 0:03:51homeless, together beneath the dome of St Paul's.So now, together, we
0:03:51 > 0:03:59remember and reflect.Some politicians from Kensington were
0:03:59 > 0:04:08asked not to come today. Emotions are still too raw.Don't come and
0:04:08 > 0:04:14look at taking selfies.No, we want people to know what has happened.
0:04:14 > 0:04:19Using voices from the time, the lingering agony of the Grenfell
0:04:19 > 0:04:24tragedy was dropped into the calm of the Cathedral.We need to feel what
0:04:24 > 0:04:29they have felt.It has let us down, this borough.So many questions and
0:04:29 > 0:04:38no answers.Today we ask why warnings were not heeded, why a
0:04:38 > 0:04:43community was left feeling neglected, and cared for, -- uncared
0:04:43 > 0:04:50for, not listened to.In a service rich with imagery, a commitment was
0:04:50 > 0:04:56maimed to turn Grenfell from a symbol of sorrow to a symbol of the
0:04:56 > 0:05:02time we learned to listen and to love. Schoolchildren scattered green
0:05:02 > 0:05:13hearts at the feet of faith leaders.
0:05:13 > 0:05:17Six months after that fateful day, the powerful were once again forced
0:05:17 > 0:05:25to look directly into the eyes of those whose trust was betrayed.It's
0:05:25 > 0:05:42like yesterday. The pain is deep... We shall not forget.For three
0:05:42 > 0:05:45centuries and Morecambe St Paul's has marked the highs and lows of
0:05:45 > 0:05:53capital. The data that list was added Grenfell. A tragedy that awoke
0:05:53 > 0:05:59London to the injustice hidden in plain sight -- two-day to that list
0:05:59 > 0:06:02was added Grenfell.
0:06:05 > 0:06:08Khadijah Saye was a promising young artist who died in Grenfell Tower.
0:06:08 > 0:06:16Her mother, Mary Mendy, was also killed in the tragedy.
0:06:16 > 0:06:18Today, members of their family were among those who travelled
0:06:18 > 0:06:20to St Paul's, to take part in today's service.
0:06:20 > 0:06:27Our special correspondent Lucy Manning spent the day with them.
0:06:27 > 0:06:32The Mendy family gather, but while the months have passed, the family's
0:06:32 > 0:06:36serviced haven't. They lost Mary Mendy, and their daughter, Khadija
0:06:36 > 0:06:41Saye, a rising star in the art world.Some people wanted her to be
0:06:41 > 0:06:44a doctor, but she didn't want to be a doctor, she wanted to be an
0:06:44 > 0:06:50artist.I cry every day, for my sister and my niece, because they
0:06:50 > 0:06:54are the only thing I have come I don't have nothing, nothing.They
0:06:54 > 0:07:00took out the best members of our family.They did.The best people in
0:07:00 > 0:07:07our family, especially Khadijah. From the youngest of their family,
0:07:07 > 0:07:13just three months old, they all came to St Paul's to stand with the other
0:07:13 > 0:07:18families, to remember with them, to cry with them. They talked to Prince
0:07:18 > 0:07:21William about the art Khadijah had produced, the prolific artist she
0:07:21 > 0:07:27would have become. This was Khadijah last year, talking about a future
0:07:27 > 0:07:35that was never hers.I can't be struggling, I need to actually
0:07:35 > 0:07:39progress and see how to make it a career, because that is the dream,
0:07:39 > 0:07:46isn't it?What was lost at Grenfell, not just a talented artist, but the
0:07:46 > 0:07:50architecture graduate, the engineering student, the taxi
0:07:50 > 0:07:56driver, the teaching assistant, the bride-to-be, the girl taking her
0:07:56 > 0:07:59GCSEs, and, of course, all the young children, with their lives in front
0:07:59 > 0:08:08of them.It was very emotional. Emotional.Emotional, yes, very
0:08:08 > 0:08:11emotional, and without that it was something she would have loved,
0:08:11 > 0:08:16because she was very religious and attended church regularly.How would
0:08:16 > 0:08:23you like people to think of Khadijah?To think of her smile, a
0:08:23 > 0:08:25soft, kind-hearted, great young woman who would have become somebody
0:08:25 > 0:08:31full stopMarion lived with them in Grenfell for a four U years before
0:08:31 > 0:08:35the fire but her aunt, cousin, and 69 others weren't safe in their own
0:08:35 > 0:08:45homes. They took the flowers from the memorial to Mary Mendy's grave.
0:08:45 > 0:08:47For one day, everyone remembered Grenfell. Her family will never
0:08:47 > 0:08:53forget.For now, we just want to know why, because they died
0:08:53 > 0:08:59needlessly. They didn't need to die. Lucy Manning, BBC News.
0:08:59 > 0:09:02The Scottish Government has said it's going to raise
0:09:02 > 0:09:08taxes for higher earners.
0:09:08 > 0:09:10Those earning more than £24,000 will pay 21
0:09:10 > 0:09:12pence in the pound - that's a higher rate
0:09:12 > 0:09:14than in the rest of the UK.
0:09:14 > 0:09:17The plan was unveiled in the draft budget this afternoon but there's
0:09:17 > 0:09:20also a new starting rate of tax, which will benefit lower earners.
0:09:20 > 0:09:22Let's cross to our Scotland Editor, Sarah Smith,
0:09:22 > 0:09:24this is quite a change...
0:09:24 > 0:09:29Yes, it is a big change, and it is the first time the Scottish
0:09:29 > 0:09:32Government have used their powers to change income tax rates in Scotland.
0:09:32 > 0:09:35They have now created a tax regime that looks really quite different to
0:09:35 > 0:09:40the rest of the UK. There are five tax bands, a lower starting rate
0:09:40 > 0:09:45than the rest of Britain and a higher top rate. And by cutting
0:09:45 > 0:09:48taxes for most Scottish workers, the government hopes they can increase
0:09:48 > 0:09:52revenues whilst not losing public support.
0:09:52 > 0:09:57An early Christmas present was delivered to many Scottish taxpayers
0:09:57 > 0:10:02today as more than two thirds will pay less income tax next year. All
0:10:02 > 0:10:05of these MSPs posing in their festive jumpers they will have to
0:10:05 > 0:10:11pay higher taxes. The Scottish Government will in crease public
0:10:11 > 0:10:15spending and give public sector workers a 3% pay rise.It overturns
0:10:15 > 0:10:21the Tory cut, it delivers an additional £4 million to the health
0:10:21 > 0:10:26service without damaging other vital services. It protects the vast
0:10:26 > 0:10:31majority of taxpayers. It is a budget for fairness and for growth.
0:10:31 > 0:10:36A new starter rate of 19% mean those earning less than £24,000 will be
0:10:36 > 0:10:41£20 better off than taxpayers and the rest of the UK. An intermediate
0:10:41 > 0:10:47rate of 21% mean somebody earning £33,000 will be £70 worse off,
0:10:47 > 0:10:52increasing the higher rate to 41% means anyone earning £60,000 will be
0:10:52 > 0:10:58£755 worse off. Putting up the additional rate to 46% will see
0:10:58 > 0:11:06those earning over £150,000 pay £1774 more than those outside
0:11:06 > 0:11:11Scotland, raising an extra £164 million for the Scottish Government.
0:11:11 > 0:11:16The Conservatives say the tax cuts will deliver only £20 more to lower
0:11:16 > 0:11:21earners while some will pay far more.Before the smoke and mirrors,
0:11:21 > 0:11:25we have had all of Scotland's business organisation saying we are
0:11:25 > 0:11:30raising taxes, it would damage Scotland's economy and growth.The
0:11:30 > 0:11:34new Scottish tax rates create winners and losers. As a public
0:11:34 > 0:11:39sector worker, he will get a tax cut, a pay rise.We definitely need
0:11:39 > 0:11:48to address this issue in the UK. Wages have gone down by about 20% in
0:11:48 > 0:11:50terms of buying power.Business owner Sharon wants to know that
0:11:50 > 0:11:56higher taxes will be spent wisely.I think if we are confident and trust
0:11:56 > 0:12:00that it will be used for the services -- services the public
0:12:00 > 0:12:04want, we need more money but there are so many needs it needs to go to
0:12:04 > 0:12:09and I am not confident it is going to the right needs.A lawyer, Alan
0:12:09 > 0:12:12is one who will be paying more. Are you personally have yet to be paying
0:12:12 > 0:12:19higher tax rates?Yes, I am, it is entirely reasonable to pay higher
0:12:19 > 0:12:22rates, it is a question of how much but yes I would certainly pay more
0:12:22 > 0:12:26tax.Figures released today show the Scottish economy is forecast to grow
0:12:26 > 0:12:31more slowly than the rest of the UK, but public spinning in Scotland will
0:12:31 > 0:12:35be significantly higher. Sarah Smith, BBC News, Edinburgh.
0:12:35 > 0:12:37Four people have died after a train collided
0:12:37 > 0:12:40with a school bus in the south of France this afternoon.
0:12:40 > 0:12:4319 others have been injured - seven seriously.
0:12:43 > 0:12:50The bus was put the carrying children aged between 11 and 15.
0:12:50 > 0:12:52It was hit by a train at a level crossing
0:12:52 > 0:12:53at Millas, near Perpignon.
0:12:53 > 0:12:57Emergency services are at the scene.
0:12:57 > 0:13:00Theresa May has arrived at a crucial Brexit summit in Brussels saying
0:13:00 > 0:13:02she's disappointed after last night's Commons defeat.
0:13:02 > 0:13:04But she said the vote - which gives parliament a say
0:13:04 > 0:13:06over the final deal - would not stop her
0:13:06 > 0:13:07delivering Brexit.
0:13:07 > 0:13:10Questions have been raised about whether her authority has been
0:13:10 > 0:13:12dented just as EU leaders prepare to move the negotiations
0:13:12 > 0:13:13into a second phase.
0:13:13 > 0:13:22Here's our Political Editor Laura Kuenssberg.
0:13:22 > 0:13:25Her job tonight, to get 27 countries of all political colours onside, the
0:13:25 > 0:13:38day after failing to line up everyone in her own party.
0:13:40 > 0:13:43We are on course to deliver on Brexit. Last week President Juncker
0:13:43 > 0:13:51said sufficient progress had been used.Do you accept as Prime
0:13:51 > 0:14:02Minister he will have to make more compromises with your own side?We
0:14:02 > 0:14:11have had 36 votes on the EU withdrawal bill and won 35.You come
0:14:11 > 0:14:20from as more?We have won 35 out of 36 votes.Give and take at home? Not
0:14:20 > 0:14:22quite. The broad where she has had two
0:14:22 > 0:14:27Quad --
0:14:27 > 0:14:30But, abroad, where she has had to come from ice,
0:14:30 > 0:14:32her cheery counterparts in a mixture of sympathy, and demand.
0:14:32 > 0:14:34This makes it even shorter, for Theresa May's Government,
0:14:34 > 0:14:37to make proposals, because if, afterwards, she needs to get
0:14:37 > 0:14:42an agreement in London, that does not help a lot.
0:14:42 > 0:14:44I have absolute faith in faith and confidence in her,
0:14:44 > 0:14:47that she speaks for the UK, and that as long as that
0:14:47 > 0:14:49is the case, as long as she is Prime Minister,
0:14:49 > 0:14:52we will deal with her, and treat her as if she has
0:14:52 > 0:14:53an overall majority.
0:14:53 > 0:14:56She is holding her cards close to her heart at the moment,
0:14:56 > 0:14:58which I understand, on the next phase.
0:14:58 > 0:15:00And this is probably a wise negotiating tactic.
0:15:00 > 0:15:03It is now for the UK to make up its mind and then together,
0:15:03 > 0:15:05to collectively see where we can get to.
0:15:05 > 0:15:12The closest friends maybe not quite convinced.
0:15:12 > 0:15:14We have made progress with Great Britain,
0:15:14 > 0:15:16said the German leader, but some questions are still open.
0:15:16 > 0:15:19Where Brexit is being brokered, May's promises of "Strong
0:15:19 > 0:15:24and Stable" seem long ago, some Tories furious their colleagues
0:15:24 > 0:15:26sent the Prime Minister to her seat after defeat.
0:15:26 > 0:15:29But, for the rebels and their new found friends in the opposition,
0:15:29 > 0:15:30listening would add authority.
0:15:30 > 0:15:32She has caused this problem for herself, actually
0:15:32 > 0:15:38what she should now do is embrace what happened last night and say,
0:15:38 > 0:15:41yes, I will involve Parliament, and then it would be obvious
0:15:41 > 0:15:43in the negotiations that I have the support of Parliament
0:15:43 > 0:15:45in what I am doing.
0:15:45 > 0:15:48barring last-minute disaster, the rest of the EU is to agree that
0:15:48 > 0:15:53Britain can move onto the next phase of our long goodbye, but Theresa May
0:15:53 > 0:15:57will enter that, knowing that the other countries provide 27 items on
0:15:57 > 0:16:02our list of problems, but parliament is perhaps the 28th, and the
0:16:02 > 0:16:06trickiest of all. Remember, tomorrow's expected agreement is
0:16:06 > 0:16:11only a promise to move onto talks about the long-term relationship.
0:16:11 > 0:16:15That home, and here, there are still an awful lot to be worked out. Laura
0:16:15 > 0:16:21Kuenssberg, BBC News, Brussels.
0:16:21 > 0:16:23The time is 16 minutes past six.
0:16:23 > 0:16:28Our top story this evening:
0:16:28 > 0:16:30Six months on, the victims of the Grenfell fire are remembered
0:16:30 > 0:16:33at a service at St Paul's.
0:16:33 > 0:16:34And still to come...
0:16:34 > 0:16:37England needed something special in the vital third test in Perth -
0:16:37 > 0:16:41Dawid Malan delivers.
0:16:41 > 0:16:44Coming up on Sportsday on BBC News, a three-month suspension for
0:16:44 > 0:16:46Britain's most successful female flat jockey, after Hayley Turner
0:16:46 > 0:16:51broke the rules on betting.
0:17:01 > 0:17:03Rupert Murdoch, whose huge media empire spans the globe -
0:17:03 > 0:17:06including interests here in Britain - has decided to sell most of it
0:17:06 > 0:17:11to the Disney Corporation.
0:17:11 > 0:17:12The deal, worth nearly £40 billion,
0:17:12 > 0:17:15ends nearly five decades of expansion that saw Mr Murdoch
0:17:15 > 0:17:18become one of the the world's most influential media figures.
0:17:18 > 0:17:20So why has he done it?
0:17:20 > 0:17:24Our Media Editor Amol Rajan reports.
0:17:24 > 0:17:27When Rupert Murdoch bought the News Of The World in 1968,
0:17:27 > 0:17:29he was an outsider.
0:17:29 > 0:17:31But this canny Australian with news in his veins made his way
0:17:31 > 0:17:34to the heart of the establishment in both Britain and America,
0:17:34 > 0:17:36wielding extraordinary influence.
0:17:36 > 0:17:41From his base in tabloid newspapers, he moved aggressively to film
0:17:41 > 0:17:42and television, owning studios and networks that entertained
0:17:42 > 0:17:46hundreds of millions of people.
0:17:46 > 0:17:51Well, I'll always have my crank calls.
0:17:51 > 0:17:54But now, in a move foreseen in The Simpsons, another Murdoch
0:17:54 > 0:17:56product, Fox has become a division of Disney.
0:17:56 > 0:17:57In a phone conference today, Rupert Murdoch
0:17:57 > 0:18:00explained his strategy.
0:18:00 > 0:18:04I know a lot of people are wondering why did the Murdochs come to such
0:18:04 > 0:18:05a momentous decision.
0:18:05 > 0:18:06I will be retreating.
0:18:06 > 0:18:08Absolutely not.
0:18:08 > 0:18:15We are pivoting at a pivotal moment.
0:18:15 > 0:18:22Andrew Neil was at Murdoch's side as an editor and executive the years.
0:18:22 > 0:18:25For him, this is the end of a dynasty.
0:18:25 > 0:18:31He's been trying to do that for 35, 40 years. He used to talk about a
0:18:31 > 0:18:35Murdoch dynasty, about putting his children into key positions, letting
0:18:35 > 0:18:40them fight for the top position and whoever wins would take over. And
0:18:40 > 0:18:49the Murdoch name would go on forever, and here at a stroke he is
0:18:49 > 0:18:54unbundling the empire.If the deal goes through it will create a new
0:18:54 > 0:19:01media superpower. Mr Murdoch is selling his world famous studio 21st
0:19:01 > 0:19:09Century Fox, television businesses including Sky. Cable networks are
0:19:09 > 0:19:18just FX and National Geographic, and Hulu which could rival Netflix. And
0:19:18 > 0:19:22that's the key for Disney. Streaming has changed broadcasting forever,
0:19:22 > 0:19:27allowing you at home to watch a seemingly infinite number of shows
0:19:27 > 0:19:33how, where, and when you want. Streaming services such as Hulu cut
0:19:33 > 0:19:37out the middleman of television stations, broadcasting directly into
0:19:37 > 0:19:43millions of homes.As the Fox international footprint has some
0:19:43 > 0:19:47extremely high-end technology to deliver this content to consumers in
0:19:47 > 0:19:51more modern ways, Sky in Europe is a good example of that, and so to the
0:19:51 > 0:19:55consumer not only will they be getting more high-quality content
0:19:55 > 0:20:02but they will be getting it in ways they demand.Sky News and Sky Sports
0:20:02 > 0:20:08look set to continue, while Fox says its own bid remains in place. Even
0:20:08 > 0:20:12with this acquisition, Disney is playing catch up with tech giants
0:20:12 > 0:20:16like Facebook, who if they aren't there already are coming to a small
0:20:16 > 0:20:22screen near you.
0:20:22 > 0:20:25Three Eastern European men who faced being deported from the UK,
0:20:25 > 0:20:27after being found sleeping rough, have won a High Court battle
0:20:27 > 0:20:30with the government.
0:20:30 > 0:20:32A judge ruled that the policy, enforced by the Home
0:20:32 > 0:20:34Office, was unlawful.
0:20:34 > 0:20:36Campaigners say the decision will affect hundreds of other rough
0:20:36 > 0:20:46sleepers facing removal, as Frankie McCamley now reports.
0:20:46 > 0:20:50Sheltering from the cold, sleeping on park benches and taking cover in
0:20:50 > 0:20:55doorways - homelessness has been on the rise in the UK for years. Its
0:20:55 > 0:20:59position this man found himself in after moving from Bulgaria in the
0:20:59 > 0:21:05hope of a better life.In Bulgaria it is really hard to get a job...He
0:21:05 > 0:21:09secured work but lost his home. Under the Government's policy this
0:21:09 > 0:21:14meant he lost his right to freedom of movement so was taken to a
0:21:14 > 0:21:20deportation centre for seven months until being released this year.I
0:21:20 > 0:21:27just a in my room, I don't go anywhere. I stay in my room. I just
0:21:27 > 0:21:33think my life is finished.Today the High Court ruled this policy of
0:21:33 > 0:21:38removing EU citizens is unlawful. Mr Justice Lang said the measure was
0:21:38 > 0:21:43discriminatory and contrary to EU law. It was Solicitor Paul Heron who
0:21:43 > 0:21:47represented a number of EU nationals who claimed their rights were being
0:21:47 > 0:21:53abused.The court accepted that being a rough sleeper in and of
0:21:53 > 0:21:58itself is not an abuse of treaty rights. The court accepts that in
0:21:58 > 0:22:02many cases, the people who have been detained and removed were often
0:22:02 > 0:22:06working in the UK but they were just in low-paid jobs and couldn't afford
0:22:06 > 0:22:11the high skyrocketed rent.In a statement the Home Office said it
0:22:11 > 0:22:14was disappointed by the outcome and will consider carefully what steps
0:22:14 > 0:22:22are necessary will reflect the future enforcement. It's not clear
0:22:22 > 0:22:25how many rough sleepers there are nationwide but in London numbers
0:22:25 > 0:22:29have fallen in the past few months with a significant drop in those
0:22:29 > 0:22:33from Eastern Europe. Campaigners believe the decision will affect
0:22:33 > 0:22:37hundreds of people currently sleeping rough, but with Brexit
0:22:37 > 0:22:40negotiations ongoing it is not clear what the implications of this
0:22:40 > 0:22:45judgment will be in the future.
0:22:45 > 0:22:49British doctors say they've made a significant break-through
0:22:49 > 0:22:51in the treatment of haemophilia A, the most common form.
0:22:51 > 0:22:53Around 2,000 people in the UK have the genetic defect
0:22:53 > 0:22:55which means their blood cannot clot properly.
0:22:55 > 0:23:04The research team used gene therapy to correct the defect
0:23:04 > 0:23:08in a small group of patients - none of them need treatment any more.
0:23:08 > 0:23:11Now there needs to be a large scale trial as our Health Correspondent
0:23:11 > 0:23:12James Gallagher reports.
0:23:12 > 0:23:14Walking to work should be simple, but it was
0:23:14 > 0:23:15unthinkable for Jake Omer.
0:23:15 > 0:23:18Haemophilia A meant even the impact of his feet on the pavement led
0:23:18 > 0:23:19to bleeding in his joints.
0:23:19 > 0:23:20But no longer.
0:23:20 > 0:23:22I think the gene therapy has hopefully given me
0:23:22 > 0:23:24a new lease of life.
0:23:24 > 0:23:27It's going to allow me, as my boys grow up, to be a lot
0:23:27 > 0:23:29more active with them, so kick footballs around,
0:23:29 > 0:23:32climb trees with them, to hopefully run around in the park
0:23:32 > 0:23:34with them, and not be someone who has got to worry
0:23:34 > 0:23:35about what I'm doing.
0:23:35 > 0:23:37Haemophilia A is a hereditary condition that stops
0:23:37 > 0:23:38the blood clotting.
0:23:38 > 0:23:41Jake was one of 13 patients given gene therapy last year.
0:23:41 > 0:23:45All of them are now off their haemophilia medication.
0:23:45 > 0:23:48This is how it works.
0:23:48 > 0:23:51Haemophilia A is caused by a defect in patients' DNA.
0:23:51 > 0:23:55So scientists made a genetically modified virus.
0:23:55 > 0:24:00It contains the healthy DNA patients are missing.
0:24:00 > 0:24:03When the virus infects the liver, it leaves the DNA behind and it
0:24:03 > 0:24:06gives the liver the instructions for making proteins called factor
0:24:06 > 0:24:10VIII that clot the blood.
0:24:10 > 0:24:13If this is how much factor VIII you or I produce,
0:24:13 > 0:24:17well this is how much is produced in a haemophilia patient.
0:24:17 > 0:24:19But you can see, after the gene therapy trial, it's almost
0:24:19 > 0:24:23up to normal.
0:24:23 > 0:24:24This is huge.
0:24:24 > 0:24:26It's groundbreaking.
0:24:26 > 0:24:28Because the option to think about normalising levels in patients
0:24:28 > 0:24:33with severe haemophilia is absolutely mind blowing.
0:24:33 > 0:24:36To offer people the potential of a normal life, when they've had
0:24:36 > 0:24:38to inject themselves with factor VIII every other day to prevent
0:24:38 > 0:24:42bleeding is transformational.
0:24:42 > 0:24:46Large studies will now take place to see if gene therapy can replace
0:24:46 > 0:24:47these regular injections and truly transform the lives
0:24:47 > 0:24:51of thousands of patients.
0:24:51 > 0:24:56James Gallagher, BBC News.
0:24:56 > 0:25:00Cricket now, and England have fought back on the first day of the vital
0:25:00 > 0:25:04third test in Perth.
0:25:04 > 0:25:08Australia are already 2-0 up in the series,
0:25:08 > 0:25:11and England need at least a draw to keep their Ashes hopes alive.
0:25:11 > 0:25:13Andy Swiss reports from Perth.
0:25:13 > 0:25:16They've been waiting a long time for this.
0:25:16 > 0:25:19After watching collapses, calamities and controversies,
0:25:19 > 0:25:22at last for England fans a bit of cricketing cheer.
0:25:22 > 0:25:25Not that it necessarily seemed that way at first.
0:25:25 > 0:25:31England opted to bat.
0:25:31 > 0:25:33But in Alastair Cook's case, not for long, out for just seven.
0:25:33 > 0:25:35As Australia's bowlers
0:25:35 > 0:25:36set about making life decidedly uncomfortable
0:25:36 > 0:25:40they broke Mark Stoneman's helmet and soon it seems England's hopes.
0:25:40 > 0:25:42Stoneman gone controversially for 56.
0:25:42 > 0:25:44The video umpire deciding it had just brushed his glove,
0:25:44 > 0:25:48to England's frustration.
0:25:48 > 0:25:54At 131-4 it seemed another tale of what if.
0:25:54 > 0:25:56But in the nick of time a centurion emerged from the ranks.
0:25:56 > 0:25:58The unheralded Dawid Malan.
0:25:58 > 0:26:01Yes, he rode his luck, dropped on 92, but together
0:26:01 > 0:26:07with Jonny Bairstow he made Australia pay.
0:26:07 > 0:26:09What a time to score your first test hundred.
0:26:09 > 0:26:13If the day belonged to England, the moment was all of his.
0:26:13 > 0:26:14COMMENTATOR:Magnificent effort.
0:26:14 > 0:26:18It was so emotional.
0:26:18 > 0:26:21I didn't really know what to do and when I got the hundred
0:26:21 > 0:26:24I was so emotional I almost started crying, to be honest,
0:26:24 > 0:26:25when it happened.
0:26:25 > 0:26:28Just when they needed it, England's best day of the series so far.
0:26:28 > 0:26:31There's still a long way to go in this match, but they've given
0:26:31 > 0:26:33themselves a chance.
0:26:33 > 0:26:36In a series so far defined by disappointment, England will hope
0:26:36 > 0:26:37this just might be a turning point.
0:26:37 > 0:26:43Andy Swiss, BBC News, Perth.
0:26:43 > 0:26:44Time for a look at the weather.
0:26:44 > 0:26:47Here's Darren Bett.
0:26:52 > 0:26:56Not quite Ashes sunshine but we had some blue skies in some areas today.
0:26:56 > 0:27:01A decent day through much of the Midlands, East Anglia and the
0:27:01 > 0:27:05south-east of England but it was an all or nothing sort of dates. There
0:27:05 > 0:27:09were showers, snow over high ground and we have the covering of snow
0:27:09 > 0:27:15still across parts of the country. Some bands of wet weather moving
0:27:15 > 0:27:20down, this one heading towards the Midlands. That first band of rain,
0:27:20 > 0:27:24sleet and hill snow tends to peter out, the next one follows on its
0:27:24 > 0:27:29heels and when we break up the cloud across the northern parts of the UK.
0:27:29 > 0:27:33Temperatures hovering close to freezing and the threat of some icy
0:27:33 > 0:27:41patches too. By tomorrow it's a northerly wind which means changes
0:27:41 > 0:27:45in the distribution of showers, which means more cloud and showers
0:27:45 > 0:27:49in the eastern part of England. Wintry showers and the northerly
0:27:49 > 0:27:53wind across northern Scotland but further south we will enjoy some
0:27:53 > 0:27:57sunshine. A bit of an edge to the wind, temperature is similar to
0:27:57 > 0:28:02today. As the wind eases off tomorrow night, look at those
0:28:02 > 0:28:05temperatures tumbling. We see a frost developing widely and it could
0:28:05 > 0:28:10be a sharp frost for the start of the weekend. We start the weekend
0:28:10 > 0:28:14with cold air but slowly it will be replaced by mild air coming in from
0:28:14 > 0:28:21the Atlantic but that change doesn't happen overnight. It will be quite
0:28:21 > 0:28:24cold down the eastern side of the UK, even though we have sunshine on
0:28:24 > 0:28:27Saturday. The south-west in particular seeing more cloud and
0:28:27 > 0:28:32some showery bursts of rain. It's probably in the second half of the
0:28:32 > 0:28:35weekend we get the stronger westerly winds, lifting the